Report on three cases and review of literature

Portal biliopathy is defined as biliary abnormalities associated most commonly with extrahepatic portal vein obstruction. We report on three cases of portal biliopathy collected within the past 15 years. All three cases were presented with variceal blee ding due to portal hypertension. Clinical signs of subsequent portal biliopathy appeared as biliary obstruction with jaundice. All patients were treated endoscopically with dilation and duodeno-biliary sten ting with a long-term favourable effect. Review of literature on clinical features, diagnostic and therapeutic options and possible complications of portal biliopathy is provided. Portal biliopathy should always be considered in the event of biliary obstruction in patients with extrahepatic portal vein obstruction. Portal biliopathy might be complicated with bile duct stones and/or cholangitis. ERCP is the method of choice both for diagnosis and treatment.